Jornal Vascular Brasileiro
http://www.jvb.periodikos.com.br/article/doi/10.1590/1677-5449.202301501
Jornal Vascular Brasileiro
Relato de Caso

Relato de caso: aorta dorsal dupla persistente

Case report: persistent double dorsal aorta

Paulo Henrique Alves Togni Filho; Ernani Alves de Oliveira; Eduardo Milani Mora; Paulo Eduardo Borher Moreira; Bruno Previdelli Coghi; Guilherme Augusto Paro

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Resumo

A aorta dorsal dupla persistente é uma anomalia congênita extremamente rara, com apenas 13 casos publicados até o presente momento. Este estudo tem como objetivo apresentar a variação embriológica observada em aorta abdominal do paciente. A descrição anatômica foi realizada a partir da revisão de prontuário eletrônico e exames de imagem. Desta forma, o presente caso refere-se a um paciente idoso de 79 anos admitido em atendimento hospitalar por queixa de dor em membro inferior esquerdo ao repouso. Foi solicitada a internação do mesmo, assim como exames laboratoriais e de imagem. Obtida como um achado de imagem a partir de angiotomografia, a variação consiste na completa separação em duas porções: uma ventral e outra dorsal, de calibres diferentes, da aorta abdominal, ao nível da terceira vértebra lombar. Isso ocorre em conjunto com a origem anômala da artéria mesentérica inferior.

Palavras-chave

variação anatômica, aorta abdominal, tomografia computadorizada, anomalia congênita

Abstract

Persistent double dorsal aorta is an extremely rare congenital anomaly, with only 13 cases published to date. The objective of this study is to present this embryological variant as observed in the abdominal aorta of a patient. The anatomical description was written up on the basis of a review of electronic medical records and imaging exams. The patient in this case was an elderly 79-year-old man who presented at emergency with pain at rest in the left lower limb. He was admitted and laboratory tests and imaging exams were ordered. The variation was an imaging finding observed on angiotomography, consisting of complete separation of the abdominal aorta into two portions - a ventral and a dorsal, with different calibers – at the level of the third lumbar vertebra. There was also an anomalous origin of the inferior mesenteric artery.

Keywords

anatomic variant; abdominal aorta; computed tomography; congenital anomaly

Referências

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Submetido em:
10/10/2023

Aceito em:
21/02/2024

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